Research of Ornithine Carbamoyltransferase Deficiency has been linked to Hyperammonemia, Urea Cycle Disorders, Inborn, Inborn Errors Of Metabolism, Comatose, Encephalopathies. The study of Ornithine Carbamoyltransferase Deficiency has been mentioned in research publications which can be found using our bioinformatics tool below. Researched pathways related to Ornithine Carbamoyltransferase Deficiency include Urea Cycle, Excretion, Transport, Pathogenesis, Fatty Acid Oxidation. These pathways complement our catalog of research reagents for the study of Ornithine Carbamoyltransferase Deficiency including antibodies and ELISA kits against SPARSE FUR, CPS, CARBAMYL PHOSPHATE SYNTHETASE I, AMINO-ACID N-ACETYLTRANSFERASE, ADSL.
Top Research Reagents
We have 1449 products for the study of Ornithine Carbamoyltransferase Deficiency that can be applied to Flow Cytometry, Immunocytochemistry/ Immunofluorescence, Immunohistochemistry, Western Blot from our catalog of antibodies and ELISA kits.
Ornithine Carbamoyltransferase Deficiency is also known as ornithine carbamoyltransferase deficiency, ornithine transcarbamylase deficiency, otc deficiency, ornithine carbamoyltransferase deficiency disease, deficiency of citrulline phosphorylase, malnutrition, otcd.
![Western Blot: Choline Acetyltransferase/ChAT Antibody [NBP1-30052] - The decrease in protein expressions of c-kit, Choline Acetyltransferase/ChAT, nNOS and Cx43 in the colon of elderly humans. Expressions of c-kit, ChAT, nNOS and Cx43 proteins in colonic muscle layers detached from youth and older adults were examined by western blotting (n=4 per group), and similar reduction was observed. Image collected and cropped by CiteAb from the following publication (//pubmed.ncbi.nlm.nih.gov/30530917/) licensed under a CC-BY license.](https://images.novusbio.com/fullsize/Choline Acetyltransferase-ChAT Antibody-Western Blot-NBP1-30052-img0006.jpg)
![Immunocytochemistry/Immunofluorescence: Choline Acetyltransferase/ChAT Antibody [NBP1-30052] - Representative images of lumbar spinal cord sections at 130 days immunostained with Choline Acetyltransferase/ChAT. Scale bar, 200 um. Image collected and cropped by CiteAb from the following publication (https://embomolmed.embopress.org/lookup/doi/10.15252/emmm.201808888), licensed under a CC-BY license.](https://images.novusbio.com/fullsize/Choline-Acetyltransferase-ChAT-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-30052-img0005.jpg)
![Immunohistochemistry-Paraffin: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Staining in human adrenal gland and liver tissues using anti-QPCT antibody. Corresponding QPCT RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Glutaminyl-peptide-Cyclotransferase-QPCT-Antibody-Immunohistochemistry-Paraffin-NBP1-81838-img0010.jpg)
![Western Blot: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Analysis in human cell line SK-MEL-30.](https://images.novusbio.com/fullsize/Glutaminyl-peptide-Cyclotransferase-QPCT-Antibody-Western-Blot-NBP1-81838-img0006.jpg)
![Immunohistochemistry-Paraffin: Fibrillin 1 Antibody [NBP1-84722] - Staining in human cervix, uterine and cerebral cortex tissues . Corresponding FBN1 RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Fibrillin-1-Antibody-Immunohistochemistry-Paraffin-NBP1-84722-img0017.jpg)
![Immunocytochemistry/Immunofluorescence: Fibrillin 1 Antibody [NBP1-84722] - Staining of human cell line U-251 MG shows localization to cytosol. Antibody staining is shown in green.](https://images.novusbio.com/fullsize/Fibrillin-1-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-84722-img0018.jpg)
![Western Blot: UMPS Antibody [NBP1-85896] - Analysis in U2OS cells transfected with control siRNA, target specific siRNA probe #1 and #2. Remaining relative intensity is presented.](https://images.novusbio.com/fullsize/UMPS-Antibody-Western-Blot-NBP1-85896-img0011.jpg)
![Immunocytochemistry/Immunofluorescence: UMPS Antibody [NBP1-85896] - Staining of human cell line U-2 OS shows localization to cytosol. Antibody staining is shown in green.](https://images.novusbio.com/fullsize/UMPS-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-85896-img0008.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining in human liver and kidney tissues . Corresponding OTC RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0020.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining of human cerebral cortex, kidney, liver and small intestine using Anti-OTC antibody NBP1-87408 (A) shows similar protein distribution across tissues to independent antibody NBP1-88121 (B).](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0027.jpg)
![Immunohistochemistry-Paraffin: Argininosuccinate Lyase Antibody [NBP1-87462] - Staining in human liver and skeletal muscle tissues using NBP1-87462 antibody. Corresponding ASL RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Argininosuccinate-Lyase-Antibody-Immunohistochemistry-Paraffin-NBP1-87462-img0014.jpg)
![Immunohistochemistry-Paraffin: Argininosuccinate Lyase Antibody [NBP1-87462] - Staining of human kidney shows moderate to strong cytoplasmic positivity in cells in tubules.](https://images.novusbio.com/fullsize/Argininosuccinate-Lyase-Antibody-Immunohistochemistry-Paraffin-NBP1-87462-img0010.jpg)
![Western Blot: Argininosuccinate Synthase Antibody [NBP1-88868] - ASS1 was successfully silenced in H4-II-E-C3 cells. Image from verified customer review.](https://images.novusbio.com/fullsize/Argininosuccinate-Synthase-Antibody-Western-Blot-NBP1-88868-img0013.jpg)
![Immunocytochemistry/Immunofluorescence: Argininosuccinate Synthase Antibody [NBP1-88868] - Staining of human cell line A-431 shows localization to nucleoplasm & cytosol. Antibody staining is shown in green.](https://images.novusbio.com/fullsize/Argininosuccinate-Synthase-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-88868-img0007.jpg)
![Immunohistochemistry-Paraffin: ABCB11 Antibody [NBP1-89319] - Staining in human liver and skeletal muscle tissues . Corresponding ABCB11 RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/ABCB11-Antibody-Immunohistochemistry-Paraffin-NBP1-89319-img0009.jpg)
![Immunohistochemistry: ABCB11 Antibody [NBP1-89319] - Histopathology of ABCB11 disease. (a) Giant-cell hepatitis (arrows) with hepatocanalicular cholestasis and (b) complete absence of ABCB11/BSEP protein are typical findings in PFIC2 patients. Inset: immunohistochemical positivity of BSEP in the apical (canalicular) domain of hepatocytes in a healthy control. (a) Hematoxylin and eosin, original magnification x200. (b, inset) Immunohistochemical staining with ABCB11 Rabbit Polyclonal Antibody (NBP1-89319, Novus Biologicals, USA), original magnification x200 (b), x400 (inset). Image collected and cropped by CiteAb from the following publication (https://pubmed.ncbi.nlm.nih.gov/30148122) licensed under a CC-BY license.](https://images.novusbio.com/fullsize/ABCB11-Antibody-Immunohistochemistry-NBP1-89319-img0012.jpg)
![Immunohistochemistry-Paraffin: Dystrophin Antibody [NBP1-89953] - Staining in human skeletal muscle and tonsil tissues . Corresponding DMD RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Dystrophin-Antibody-Immunohistochemistry-Paraffin-NBP1-89953-img0010.jpg)
![Immunohistochemistry-Paraffin: Dystrophin Antibody [NBP1-89953] - Staining of human heart muscle shows strong membranous positivity in myocytes.](https://images.novusbio.com/fullsize/Dystrophin-Antibody-Immunohistochemistry-Paraffin-NBP1-89953-img0007.jpg)
![Western Blot: SEC14L2 Antibody (4H2) [NBP2-01346] Analysis of extracts (35ug) from 9 different cell lines by using anti-SEC14L2 monoclonal antibody.](https://images.novusbio.com/fullsize/SEC14L2-Antibody-4H2-Western-Blot-NBP2-01346-img0006.jpg)
![Immunocytochemistry/Immunofluorescence: SEC14L2 Antibody (4H2) [NBP2-01346] - Staining of COS7 cells transiently transfected by pCMV6-ENTRY SEC14L2.](https://images.novusbio.com/fullsize/SEC14L2-Antibody-4H2-Immunocytochemistry-Immunofluorescence-NBP2-01346-img0005.jpg)
![Western Blot: Adenylosuccinate Lyase Antibody (OTI2D10) [NBP2-03107] - Blot showing the effect of hypoxia on the protein expression levels of the purine biosynthetic enzymes. HIF-1 alpha is stabilized in hypoxia as expected, and no significant increase in the purine enzymes was detected between normoxic (21% oxygen) and hypoxic (1% oxygen) growth conditions. The positions of molecular markers surrounding each band of interest are shown for each blot. ADSL (NBP2-03107), ATIC (NBP2-01941), FGAMS (NBP1-84691), GART (H00002618-M01), HIF-1a (NB100-449), PAICS (NBP2-02817), PPAT (NBP2-02056). Image collected and cropped by CiteAb from the following publication (//pubmed.ncbi.nlm.nih.gov/32439803/) licensed under a CC-BY license.](https://images.novusbio.com/fullsize/Adenylosuccinate-Lyase-Antibody-OTI2D10-Western-Blot-NBP2-03107-img0012.jpg)
![Immunohistochemistry-Paraffin: Adenylosuccinate Lyase Antibody (OTI2D10) [NBP2-03107] - Staining of paraffin-embedded Human lymphoma tissue using anti-Adenylosuccinate Lyase mouse monoclonal antibody.](https://images.novusbio.com/fullsize/Adenylosuccinate-Lyase-Antibody-OTI2D10-Immunohistochemistry-Paraffin-NBP2-03107-img0010.jpg)
![Western Blot: Glutamine Synthetase Antibody [NB110-41404] - Analysis of glutamine synthase. 40ug of lysates from mouse (Lanes M), rat (Lane R), pig (Lane P), bovine (Lane B), or human (Lane Hu) retina were probed. A 42 kDa band was identified in lysates from retinas of all species.](https://images.novusbio.com/fullsize/Glutamine-Synthetase-Antibody-Western-Blot-NB110-41404-img0003.jpg)
![Immunocytochemistry/Immunofluorescence: Glutamine Synthetase Antibody [NB110-41404] - Immunofluorescence using NB110-41404. Submitted via verified customer review.](https://images.novusbio.com/fullsize/Glutamine-Synthetase-Antibody-Immunocytochemistry-Immunofluorescence-NB110-41404-img0006.jpg)
![Western Blot: RPGR Antibody [NBP2-93653] - Western blot analysis of extracts of Rat testis, using RPGR antibody (NBP2-93653) at 1:500 dilution. Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution. Lysates/proteins: 25ug per lane. Blocking buffer: 3% nonfat dry milk in TBST. Detection: ECL Basic Kit. Exposure time: 30s.](https://images.novusbio.com/fullsize/RPGR-Antibody-Western-Blot-NBP2-93653-img0001.jpg)
![Western Blot: RPGR Antibody [NBP2-93653] - Western blot analysis of extracts of Mouse brain, using RPGR antibody (NBP2-93653) at 1:500 dilution. Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution. Lysates/proteins: 25ug per lane. Blocking buffer: 3% nonfat dry milk in TBST. Detection: ECL Enhanced Kit. Exposure time: 180s.](https://images.novusbio.com/fullsize/RPGR Antibody-Western Blot-NBP2-93653-img0002.jpg)
![Western Blot: NAGS Antibody [NBP2-93763] - Analysis of extracts of various cell lines, using NAGS at 1:3000 dilution.Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) at 1:10000 dilution.Lysates/proteins: 25ug per lane.Blocking buffer: 3% nonfat dry milk in TBST.Detection: ECL Basic Kit .Exposure time: 90s.](https://images.novusbio.com/fullsize/NAGS-Antibody-Western-Blot-NBP2-93763-img0001.jpg)
