Research of Propionic Acidemia has been linked to Acidemia, Methylmalonic Acidemia, Inborn Errors Of Metabolism, Metabolic Diseases, Acidosis. The study of Propionic Acidemia has been mentioned in research publications which can be found using our bioinformatics tool below. Researched pathways related to Propionic Acidemia include Excretion, Urea Cycle, Transport, Fatty Acid Oxidation, Pathogenesis. These pathways complement our catalog of research reagents for the study of Propionic Acidemia including antibodies and ELISA kits against ECHDC1, PCCB, BLOC1S6, PRH2, PRH1.
Top Research Reagents
We have 1311 products for the study of Propionic Acidemia that can be applied to Flow Cytometry, Immunocytochemistry/ Immunofluorescence, Immunohistochemistry, Western Blot from our catalog of antibodies and ELISA kits.
Propionic Acidemia is also known as propionic acidemia, ketotic hyperglycinemia, ketotic glycinemia, ketotic ii glycinemia, propionic aciduria, propionicaciduria, hyperglycinemia.
![Western Blot: EPB42 Antibody (2G12) [H00002038-M01] - Analysis of EPB42 expression in transfected 293T cell line by EPB42 monoclonal antibody (M01), clone 2G12.Lane 1: EPB42 transfected lysate(69.5 KDa).Lane 2: Non-transfected lysate.](https://images.novusbio.com/fullsize/EPB42-Antibody-2G12-Western-Blot-H00002038-M01-img0005.jpg)
![Immunocytochemistry/Immunofluorescence: EPB42 Antibody (2G12) [H00002038-M01] - Analysis of monoclonal antibody to EPB42 on HeLa cell . Antibody concentration 10 ug/ml.](https://images.novusbio.com/fullsize/EPB42-Antibody-2G12-Immunocytochemistry-Immunofluorescence-H00002038-M01-img0003.jpg)
![Western Blot: PCCA Antibody [H00005095-B01P] - Analysis of PCCA expression in human liver.](https://images.novusbio.com/fullsize/PCCA-Antibody-Western-Blot-H00005095-B01P-img0004.jpg)
![Western Blot: PCCA Antibody [H00005095-B01P] - Analysis of PCCA expression in U-2 OS.](https://images.novusbio.com/fullsize/PCCA-Antibody-Western-Blot-H00005095-B01P-img0003.jpg)
![Western Blot: HMGCL Antibody [NBP1-32767] - rat liver lysate/extract 10 % SDS-PAGE gel, antibody dilution 1:10000.](https://images.novusbio.com/fullsize/HMGCL-Antibody-Western-Blot-NBP1-32767-img0007.jpg)
![Immunocytochemistry/Immunofluorescence: HMGCL Antibody [NBP1-32767] - HeLa cells were fixed in ice-cold MeOH for 5 min. Green: HMGCL protein stained by HMGCL antibody diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar = 10 um.](https://images.novusbio.com/fullsize/HMGCL-Antibody-Immunocytochemistry-Immunofluorescence-NBP1-32767-img0008.jpg)
![Western Blot: Pancreatic Amylase Alpha Antibody (6D4) [NBP1-47659] - Pancreatic Amylase Alpha Antibody (6D4) HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY Pancreatic Amylase(Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-Pancreatic Amylase.](https://images.novusbio.com/fullsize/Pancreatic-Amylase-Alpha-Antibody-6D4-Western-Blot-NBP1-47659-img0022.jpg)
![Immunohistochemistry-Paraffin: Pancreatic Amylase Alpha Antibody (6D4) [NBP1-47659] - Pancreatic Amylase Alpha Antibody (6D4) Staining of paraffin-embedded ovary using anti-Pancreatic Amylase mouse monoclonal antibody.](https://images.novusbio.com/fullsize/Pancreatic-Amylase-Alpha-Antibody-6D4-Immunohistochemistry-Paraffin-NBP1-47659-img0021.jpg)
![Immunohistochemistry-Paraffin: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Staining in human adrenal gland and liver tissues using anti-QPCT antibody. Corresponding QPCT RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Glutaminyl-peptide-Cyclotransferase-QPCT-Antibody-Immunohistochemistry-Paraffin-NBP1-81838-img0010.jpg)
![Western Blot: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Analysis in human cell line SK-MEL-30.](https://images.novusbio.com/fullsize/Glutaminyl-peptide-Cyclotransferase-QPCT-Antibody-Western-Blot-NBP1-81838-img0006.jpg)
![Immunohistochemistry-Paraffin: ACAA1 Antibody [NBP1-85786] - Analysis in human liver and pancreas tissues using NBP1-85786 antibody. Corresponding ACAA1 RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/ACAA1-Antibody-Immunohistochemistry-Paraffin-NBP1-85786-img0013.jpg)
![Western Blot: ACAA1 Antibody [NBP1-85786] - Analysis using Anti-ACAA1 antibody NBP1-85786 (A) shows similar pattern to independent antibody NBP1-86128 (B).](https://images.novusbio.com/fullsize/ACAA1-Antibody-Western-Blot-NBP1-85786-img0011.jpg)
![Immunohistochemistry-Paraffin: PCCB Antibody [NBP1-85886] - Staining in human liver and skin tissues . Corresponding PCCB RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/PCCB-Antibody-Immunohistochemistry-Paraffin-NBP1-85886-img0023.jpg)
![Immunohistochemistry-Paraffin: PCCB Antibody [NBP1-85886] - Staining of human kidney, liver, salivary gland and tonsil using Anti-PCCB antibody NBP1-85886 (A) shows similar protein distribution across tissues to independent antibody NBP1-85887 (B).](https://images.novusbio.com/fullsize/PCCB-Antibody-Immunohistochemistry-Paraffin-NBP1-85886-img0024.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining in human liver and kidney tissues . Corresponding OTC RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0020.jpg)
![Immunohistochemistry-Paraffin: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining of human cerebral cortex, kidney, liver and small intestine using Anti-OTC antibody NBP1-87408 (A) shows similar protein distribution across tissues to independent antibody NBP1-88121 (B).](https://images.novusbio.com/fullsize/Ornithine-Carbamoyltransferase-Antibody-Immunohistochemistry-Paraffin-NBP1-87408-img0027.jpg)
![Western Blot: Pallidin Antibody (1H9) [NBP2-01763] - HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY Pallidin (Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-Pallidin.](https://images.novusbio.com/fullsize/Pallidin-Antibody-1H9-Western-Blot-NBP2-01763-img0007.jpg)
![Immunohistochemistry-Paraffin: Pallidin Antibody (1H9) [NBP2-01763] - Staining of paraffin-embedded Human tonsil using anti-Pallidin mouse monoclonal antibody.](https://images.novusbio.com/fullsize/Pallidin-Antibody-1H9-Immunohistochemistry-Paraffin-NBP2-01763-img0006.jpg)
![SDS-Page: PRH1 Protein [NBP2-23368]](https://images.novusbio.com/fullsize/PRH1-Protein-SDS-Page-NBP2-23368-img0001.jpg)
![Immunohistochemistry-Paraffin: LAMC2 Antibody (CL2980) [NBP2-42388] - Staining in human fallopian tube and liver tissues. Corresponding LAMC2 RNA-seq data are presented for the same tissues.](https://images.novusbio.com/fullsize/LAMC2-Antibody-CL2980-Immunohistochemistry-Paraffin-NBP2-42388-img0023.jpg)
![Western Blot: LAMC2 Antibody (CL2980) [NBP2-42388] - Analysis in A-431 cells transfected with control siRNA, target specific siRNA probe #1 and #2, using Anti-LAMC2 antibody. Remaining relative intensity is presented. Loading control: Anti-GAPDH.](https://images.novusbio.com/fullsize/LAMC2-Antibody-CL2980-Western-Blot-NBP2-42388-img0017.jpg)
![Western Blot: ACAA2 Antibody (OTI1C10) [NBP2-46477] - Analysis of extracts (35ug) from 9 different cell lines (HepG2: human; HeLa: human; SVT2: mouse; A549: human; COS7: monkey; Jurkat: human; MDCK: canine; PC12: rat; MCF7: human).](https://images.novusbio.com/fullsize/ACAA2-Antibody-OTI1C10-Western-Blot-NBP2-46477-img0009.jpg)
![Immunohistochemistry: ACAA2 Antibody (OTI1C10) [NBP2-46477] - Analysis of Human endometrium tissue. (Heat-induced epitope retrieval by 10mM citric buffer, pH6.0, 120C for 3min)](https://images.novusbio.com/fullsize/ACAA2-Antibody-OTI1C10-Immunohistochemistry-NBP2-46477-img0007.jpg)
![Western Blot: Biotinidase/BTD Antibody [NBP2-97093] - Anti-Biotinidase/BTD rabbit polyclonal antibody at 1:500 dilution. Lane A: Jurkat Whole Cell Lysate. Lysates/proteins at 30 ug per lane. Secondary Goat Anti-Rabbit IgG H&L (Dylight 800) at 1/10000 dilution. Developed using the Odyssey technique. Performed under reducing conditions. Predicted band size: 61 kDa. Observed band size: 48 kDa](https://images.novusbio.com/fullsize/Biotinidase-BTD-Antibody-Western-Blot-NBP2-97093-img0004.jpg)
![Immunohistochemistry-Paraffin: Biotinidase/BTD Antibody [NBP2-97093] - Immunochemical staining of human Biotinidase/BTD in human liver with rabbit polyclonal antibody (1:5000, formalin-fixed paraffin embedded sections).](https://images.novusbio.com/fullsize/Biotinidase-BTD-Antibody-Immunohistochemistry-Paraffin-NBP2-97093-img0003.jpg)
![SDS-Page: Recombinant Human PRH2 Protein [H00005555-P01] - 12.5% SDS-PAGE Stained with Coomassie Blue.](https://images.novusbio.com/fullsize/qc_test-H00005555-P01-1.jpg)
![Western Blot: ECHDC1 Antibody [NBP3-12637] - Lane A: U-251MG Whole Cell LysateLysates/proteins at 30 ug per lane.SecondaryGoat Anti-Rabbit IgG (H+L)/HRP at 1/10000 dilution.Developed using the ECL technique.Performed under reducing conditions.Predicted band size:34 kDaObserved band size:34 kDa(We are unsure as to the identity of these extra bands.)](https://images.novusbio.com/fullsize/ECHDC1-Antibody-Western-Blot-NBP3-12637-img0001.jpg)
![Immunocytochemistry/Immunofluorescence: ECHDC1 Antibody [NBP3-12637] - Staining of ECHDC1 in HepG2 cells. Cells were fixed with 4% PFA, permeabilzed with 0.3% Triton X-100 in PBS,blocked with 10% serum, and incubated with rabbit anti-Human ECHDC1 polyclonal antibody (dilution ratio 1:200) at 4? overnight. Then cells were stained with the Alexa Fluor&#174;488-conjugated Goat Anti-rabbit IgG secondary antibody (green) and counterstained with DAPI (blue).Positive staining was localized to Cytoplasm.](https://images.novusbio.com/fullsize/ECHDC1-Antibody-Immunocytochemistry-Immunofluorescence-NBP3-12637-img0003.jpg)
